Etiology

  • ๊ฐœ์™€ ๊ณ ์–‘์ด ๋‘˜ ๋‹ค์—์„œ Rare type of IBD
  • Granulomatous IBD๊ฐ€ ์‚ฌ๋žŒ์˜ Crohnโ€™s Dz (ํฌ๋ก ๋ณ‘)๊ณผ ์œ ์‚ฌ.

Clinical features

  • ์•ฝ๋ฌผ ์น˜๋ฃŒ์— ๋ฐ˜์‘์ด ๋ณ„๋กœ ์—†์Œ
  • ๊ตญ์†Œ์ ์œผ๋กœ ๋ฐœ์ƒํ•˜๋ฉด ์ ˆ์ œํ•ด์•ผ ํ•  ์ˆ˜๋„ ์žˆ์Œ
  • PLE์™€ ๋น„์Šทํ•œ ์ž„์ƒ ์ฆ์ƒ
  • ์ฒด์ค‘ ๊ฐ์†Œ, ์„ค์‚ฌ

Diagnosis

  • ์กฐ์ง ๊ฒ€์‚ฌ๋กœ ์ง„๋‹จ (macrophagy๊ฐ€ ๋งŽ์Œ)

Treatment

  • ๊ตญ์†Œ์ ์ด๋ฉด ์ˆ˜์ˆ ์  ์ ˆ์ œ
  • Diffuseํ•˜๋‹ค๋ฉด ์˜ˆํ›„ ๋งค์šฐ poor, ๋ชจ๋“  ์ˆ˜๋‹จ์„ ๋™์›ํ•ด๋ณด์ž.
    • Corticosteroids
    • Azathioprine
    • Metronidazole
    • Dietary therapy

Prognosis

  • rareํ•˜์ง€๋งŒ, ์˜ˆํ›„๋Š” poor